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Research Article| Volume 14, ISSUE 5, P281-295, October 1999

Current knowledge in the management of children and adolescents with sickle cell disease: Part 1, physiological issues

  • Kathleen Simon
    Correspondence
    Address reprint requests to Kathleen Simon, DNSc, RN, College of Nursing, Medical University of South Carolina, 99 Jonathan Lucas St., Charleston, SC 29425.
    Affiliations
    College of Nursing, Medical University of South Carolina, Charleston, SC, USA

    College of Medicine, Department of Pediatrics, Medical University of South Carolina, Charleston, SC, USA
    Search for articles by this author
  • Marie L. Lobo
    Affiliations
    College of Nursing, Medical University of South Carolina, Charleston, SC, USA

    College of Medicine, Department of Pediatrics, Medical University of South Carolina, Charleston, SC, USA
    Search for articles by this author
  • Sherron Jackson
    Affiliations
    College of Nursing, Medical University of South Carolina, Charleston, SC, USA

    College of Medicine, Department of Pediatrics, Medical University of South Carolina, Charleston, SC, USA
    Search for articles by this author
DOI:https://doi.org/10.1016/S0882-5963(99)80028-1
Current knowledge in the management of children and adolescents with sickle cell disease: Part 1, physiological issues
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      This article reviews the current state of the knowledge in the management of children and adolescents with sickle cell disease (SCD). Athorough review of the literature concerning physiological issues including the clinical manifestations of SCD as well as current treatment modalities is included. Therapeutic management of health and illness for a child with SCD is discussed in relation to primary, secondary, and tertiary prevention. Recommendations for nursing practice and research are made.
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      DOI: https://doi.org/10.1016/S0882-5963(99)80028-1

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      © 1999 W.B. Sauders Company. Published by Elsevier Inc.

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